Is choledochal cyst dangerous?

There is an increased risk of cancer in the wall of the cyst. In older individuals, choledochal cysts are more likely to cause abdominal pain and intermittent episodes of jaundice and occasionally cholangitis (inflammation within the bile ducts caused by the spread of bacteria from the intestine into the bile ducts).

Is choledochal cyst curable?

The treatment of choice for choledochal cysts is complete excision of the cyst with construction of a biliary-enteric anastomosis to restore continuity with the gastrointestinal tract.

When does a choledochal cyst need surgery?

Factors to be considered when performing surgery on patients with biliary cystic disease include: (1) age, (2) presenting symptoms, (3) cyst type, (4) associated biliary stones, (5) prior biliary surgery, (6) intrahepatic strictures, (7) hepatic atrophy/hypertrophy, (8) biliary cirrhosis, (9) portal hypertension, and ( …

How is a choledochal cyst removed?

Choledochal cysts are typically treated surgically, either by an open surgical procedure (using one incision) or laparoscopically, where small incisions and a camera are used to guide the surgeon. Both procedures are performed in the operating room under general anesthesia.

How is RPC treated?

Treatment. The treatment of RPC involves management of sepsis during episodes of cholangitis with antibiotics, abscess drainage, and blood pressure support. With resistant infection, a surgical hepatectomy or hepaticocutaneousjejunostomy can be performed. Lifelong surveillance for malignancy is also usually necessary.

How does choledochal cyst cause obstruction?

Stone and protein plug formation in the distal common bile duct and pancreatic duct causes obstruction and resultant pancreatitis. Protein plug formation may be due to chronic inflammation and the formation of albumin-rich exudate or the hypersecretion of mucin from dysplastic epithelium.

How common are choledochal cysts?

Choledochal cysts are rare: one in every 100,000 to 150,000 children in Western countries is born with choledochal cysts. Girls are four times more likely to be affected than boys. The condition is more common in East Asian countries, especially Japan, though researchers do not know why.

What does RPC mean in medical terms?

Specialty. General surgery. Recurrent pyogenic cholangitis (RPC), also known as Hong Kong disease, Oriental cholangitis, and Oriental infestational cholangitis, is a chronic infection characterized by recurrent bouts of bacterial cholangitis with primary hepatolithiasis.

What is RPC in medical?

Recurrent pyogenic cholangitis (RPC) is characterized by a recurrent syndrome of bacterial cholangitis that occurs in association with intrahepatic pigment stones and intrahepatic biliary obstruction.

Are choledochal cysts hereditary?

Choledochal cyst is a rare congenital dilatation of the extrahepatic and/or intrahepatic biliary tract. Some possibilities have been postulated regarding inheritance of congenital bile duct dilatation (CBD), since several familial CBD cases have been reported. However, the etiology of CBD is essentially unknown.

What is pyogenic cholangitis?

INTRODUCTION. Recurrent pyogenic cholangitis is a disease characterized by intrabiliary pigment stone formation, resulting in stricturing of the biliary tree and biliary obstruction with recurrent bouts of cholangitis. Various other names have been used since the first description in 1930 [1].

What are the possible complications of a choledochal cyst?

There is an increased risk of cancer in the wall of the cyst. In older individuals, choledochal cysts are more likely to cause abdominal pain and intermittent episodes of jaundice and occasionally cholangitis (inflammation within the bile ducts caused by the spread of bacteria from the intestine into the bile ducts). Pancreatitis also may occur.

How are cholecholedochal cysts diagnosed?

Choledochal cysts can be diagnosed in several ways. The most common is by ultrasonography. The second most common way is by cholangiography, that is, the filling of the bile ducts with dye followed by x-ray imaging.

What happens if a liver cyst is not removed?

If the obstruction is not relieved, permanent damage may occur to the liver – scarring and cirrhosis – with the signs of portal hypertension (obstruction to the flow of blood through the liver) and ascites (fluid accumulation in the abdomen). There is an increased risk of cancer in the wall of the cyst.

What is the treatment for a cyst on the gallbladder?

Treatment of a cyst depends upon what caused the cyst in the first place. Duodenal biliary drainage is a procedure used to help diagnose gallstones. A duodenal biliary drainage procedure is fairly risk free and painless.